Paratesticular/testicular ​desmoplastic round small cell malignant tumor: case report and literature review.

Revista Colombiana de Cancerología

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Title Paratesticular/testicular ​desmoplastic round small cell malignant tumor: case report and literature review.
Tumor desmoplásico de célula pequeña y redonda paratesticular/testicular: reporte de caso y revisión de la literatura.
 
Creator Osma Charris, Handerson Rafael
Contreras Mejía, Fernando
Vallejo Yepes, Camilo
Bautista Saiz, Carolina
Medina Boada, Vilma
Roncancio Velandia, Tatiana
 
Subject Desmoplastic Small Round Cell Tumor; Sarcoma; Sarcoma, Small Cell; Sarcoma, Ewing; Testicular Neoplasms; Drug Therapy.
Tumor Desmoplásico de Células Pequeñas Redondas; Sarcoma; Sarcoma de Células Pequeñas; Sarcoma de Ewing; Quimioterapia.
 
Description Desmoplastic small round cell tumor (DSRCT) is a rare and aggressive malignant neoplastic disease. It predominantly affects men between the second and third decades of life. Patients with it have a poor prognosis, with a 5-year survival of up to 30%. It generally presents as a mass in the abdominal cavity, often multifocal. A multimodal approach is recommended for its treatment, with surgery, chemotherapy and radiotherapy. Just over 20 cases of testicular/paratesticular DSRCT have been reported in the literature. Next, we present an illustrative case in this location, the case is discussed and a review of the literature is carried out.
El tumor desmoplásico de célula redonda y pequeña (TDCRP) es una patología neoplásica maligna agresiva y poco común. Afecta predominantemente a hombres entre la segunda y tercera década de la vida. Los pacientes que la padecen tienen un pobre pronóstico, con una supervivencia global a 5 años de hasta el 30%. Se presenta generalmente como una masa en la cavidad abdominal, frecuentemente multifocal. Para su tratamiento se recomienda un enfoque multimodal, con cirugía, quimioterapia y radioterapia. Poco más de 20 casos de TDCRP a nivel testicular/paratesticular se han reportado en la literatura. A continuación, presentamos un caso ilustrativo en ésta localización, se discute el caso y se realiza revisión de la literatura.
 
Publisher Instituto Nacional de Cancerología
 
Date 2020-07-03
 
Type info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
 
Format application/pdf
 
Identifier https://www.revistacancercol.org/index.php/cancer/article/view/691
10.35509/01239015.691
 
Source Revista Colombiana de Cancerología; Vol. 24 No. 3 (2020); 125-134
Revista Colombiana de Cancerología; Vol. 24 Núm. 3 (2020); 125-134
Revista Colombiana de Cancerología; v. 24 n. 3 (2020); 125-134
2346-0199
0123-9015
 
Language spa
 
Relation https://www.revistacancercol.org/index.php/cancer/article/view/691/512
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